Frehley syndrome: hauj lwm, mob, kev kho mob, cev xeeb tub thiab yug menyuam

Anomalies txuam nrog rau mob txeeb zig account rau ntau tshaj 35% ntawm tag nrho cov congenital malformations nyob rau hauv tib neeg. Nyob rau hauv cov ntaub ntawv no, muaj mob qhov twg xws kab mob no asymptomatic thiab raug txiav txim xwb thaum lub sij hawm tiav nkauj tiav nraug los yog cev xeeb tub. Frehley syndrome - raum congenital anomaly cim uas ib tug hla ntawm pem hauv ntej thiab nram qab lub sab sauv ceg ntawm lub raum leeg. Raws li ib tug tsim nyog tau, cuam tshuam ib txwm lub cev muaj nuj nqi.

Lub npe ntawm lub syndrome lub npe hu ua tom qab ib tug American urologist, uas thawj tau piav nws. Nyob rau hauv no tsab xov xwm peb yuav txoj kev nyob rau hauv cov ua, cov tsos mob thiab kev kho mob ntawm tus kab mob no.

Yuav ua li cas yog nws?

Raws li twb tau hais, yog tias syndrome Frehley hla pem hauv ntej thiab nram qab lub ceg ntawm cov raum leeg. Nws yog ua tau rau ib nrab compression ntawm lub sab sauv qhov chaw ntawm lub plab mog los yog ureteropelvic hlws ris. Raws li ib tug tshwm sim ntawm lub raum muaj nuj nqi tej zaum yuav ua txhaum los yog txawm poob lawm. Yog yuav ua rau muaj pob zeb tsim, cov tsos ntawm tawg. Cov zis yuav yuav ntes tau ib co kua nplaum ntawm cov ntshav.

Ib tug zoo xws li cov anomaly tshwm sim txawm thaum lub sij hawm embryogenesis raum vascular system thaum yuav tso lawv txoj kev loj hlob, tab sis cov preservation ntawm cov lug.

Frehley syndrome yog laus nyob rau txoj cai thiab nyob rau sab laug, uas yog, nws feem ntau yog muaj feem xyuam rau ib raum. Nyob rau hauv huab yuav raug kev txom nyem ob lub cev. Thaum zoo li no syndrome yuav tsum tau nrog los ntawm cov kho raws sau tus sab sauv pab pawg neeg ntawm khob thiab txoj cai los yog sab laug pyeloectasia vim ureteral dab tsi thaiv.

cov tsos mob

Muaj ib co cim kov qhia tias tus neeg mob yuav tsum tau Frehley syndrome. Cov tsos mob yog hnov mob nyob rau hauv lub lumbar cheeb tsam, lub raum Colic, uas yog tam sim no nyob rau hauv kev twb kev txuas nrog ib theem nephrolithiasis. Nyob rau hauv tas li ntawd, muaj ib tug me arterial tawg, raws li zoo raws li macro- thiab me me hematuria.

mob ntawm lub syndrome

Cov feem ntau nyuaj rau ntes clinically Frehley syndrome nyob rau hauv cov tub ntxhais, tshwj xeeb tshaj yog nyob rau hauv cov me nyuam mos. Yuav kom muab tso ib tug muaj tseeb mob siv cov qauv ntawm cov doppler raum cov hlab ntsha, kuj siv multislice xoo tomography.

Cov me nyuam tsis yooj yim mus nqa tawm angiographic kev tshawb fawb, yog li ntawd lawv tam sim no tsis yog siv.

Nyob rau hauv tas li ntawd mus rau cov kev ntawm cov neeg mob tshuaj cov kev swb ntawm cov zis thiab ntshav mus kuaj, xws li xob cov tshuaj thiab muaj. Nyob rau hauv tas li ntawd, nqa tawm ultrasound ntawm lub urinary system.

kev kho mob

Kev kho mob ntawm tus kab mob no yog muab tsuas yog tom qab ceev faj complex kev soj ntsuam thiab kev paub ntawm tus mob. Conservative txoj kev - antihypertensive txoj kev kho - siv nyob rau hauv uas tsis tshua muaj mob. Nws yog qhia, raws li ib tug txoj cai, ib tug txo nyob rau hauv siab hais tias nws yog tsa. Tsis tas li ntawd ua ib tug series ntawm kev ntsuas mus tshem tawm cov theem nrab pyelonephritis thiab koom nyob rau hauv cov kev tiv thaiv ntawm urolithiasis.

Txawm li cas los, cov txaus ntseeg kawg nkaus txoj kev uas yuav tshem tawm Frehley syndrome - kev kho mob yog conservative thiab phais. Thaum lub sij hawm kev phais, tus kws kho mob tshem tawm cov hla kev ntawm cov hlab ntsha nyob rau hauv ob lub raum thiab lub siab rau lawv yog haujlwm.

Nyob rau hauv txhua rooj plaub, cov neeg mob (tshwj xeeb tshaj yog cov me nyuam) yuav tsum tau sau npe nyob rau hauv-nephrologist tus kws kho mob tsis tu ncua thiab tau txais nws lub tswv yim, coj tus tsim nyog kev ntsuam xyuas kom dhau, ultrasonic thiab radiographic kev tshawb fawb. Nyob rau hauv tom qab lub neej Frehley syndrome yuav nws tus kheej kiag li tsis qhia cov neeg kawm ntawv ntawm tsis xis nyob yog nyob ntawm seb xav clamped raum plab mog. Nrog ib tug noj qab nyob zoo txoj kev ua neej thiab lub tsis tuaj kawm ntawv ntawm tsis tau phem, cov neeg mob tej zaum yuav tsis xav tias tej yam.

cev xeeb tub

Cev xeeb tub thiab yug me nyuam ntawm ib tug me nyuam nrog cov syndrome Frehley nws niam nyob xwb nyob rau hauv lub saib xyuas ntawm ib tug tshwj xeeb. Feem ntau, cov poj niam uas congenital raum txoj kev loj hlob, uas muaj xws li active syndrome, pub mus rau tim txiv hmab txiv ntoo tsuas yog tom qab phais. Qhov tseeb hais tias Frehley lub syndrome yog feem ntau nrog los ntawm ntshav siab, cev xeeb tub nyob rau hauv cov ntaub ntawv no yog xav paub ntau loj heev, tej zaum nws yuav tsum tau tu ncua nyob rau hauv lub sij hawm tom qab 22 lub lim piam.

Tab sis txawm tom qab ib tug muaj kev vam meej cov lag luam thiab rov qab los ntawm lub raum muaj nuj nqi ntawm lub cev xeeb tub poj niam yuav tsum qhia nws obstetrician. Tag nrho lub sij hawm ntawm hnub ntawm tus me nyuam tus neeg mob yuav tsum tau yuav tsum tau tswj los ntawm ib tug nephrologist, los ntawm lub sij hawm rau lub sij hawm rau kev ntsuam xyuas, kev tshawb fawb tau qhov chaw thiab, yog tias tsim nyog, pw tsev kho mob.

Heev feem ntau ntsuas raum kab mob tej zaum yuav tshwm sim nyob rau lub sij hawm ntawm 15-16 los yog 26-30 lub lis piam. Tej yam tshwm sim yog detachable ncua zis, mob o ntawm ob txhais tes thiab ob txhais taw, mob thiab tsis xis nyob thaum lub sij hawm tso zis. Thaum ib tug tom qab hnub tim teeb meem yog tau vim lub loj hlob sai tsev me nyuam, uas txo nws hwj siab rau lub ureters. Nyob rau hauv cov ntaub ntawv ntawm tej yam tshwm sim uas cev xeeb tub syndrome Frehley yuav tsum tau ceev pw tsev kho mob.

Me nyuam nyob rau hauv syndrome Frehley

Heev feem ntau, lub raum tsis xws luag yog ib tug hais rau caesarean seem. Tab sis cov kev hem thawj rau tus me nyuam nyob rau hauv cov ntaub ntawv no yog negligible.

Rau cov poj niam nrog cov syndrome Frehley thiab lwm yam kev txawv txav ntawm ob lub raum, muaj tshwj xeeb maternity tsev kho mob nyob rau hauv lub xeev uas yog ib txwm tam sim no urology thiab Nephrology, thiab mos liab tam sim ntawd tom qab yug tus me nyuam yog nqa tawm ib qho kev daim ntawv ntsuam xyuas.

Yog li ntawd, hauv tsab xov xwm twb xam tau tias yog ib lub raum kab mob raws li Frehley lub syndrome. Txawm tias muaj tseeb hais tias cov anomaly yog ib tug congenital, tam sim no nws muaj peev xwm yuav kho tau zoo, thiab cov neeg mob tom qab phais yuav tau rov qab mus rau ib tug qub txoj kev ua neej.