Noj qab haus huv, Tshuaj
Banti lub Syndrome: Cov tsos mob, kev kho mob
"Syndrome" nyob rau hauv Greek txhais hais tias "pawg" los yog "compound". Nyob rau hauv cov tshuaj, qhov no hauj lwm yog muab cov kab mob uas muaj ib tug tej yam muaj pes tsawg tus ntawm coj los nta, feem ntau tshwm ua ke. Yog li, ua ke nrog cov nta tseeb mob yuav tsum tau hu ua ib tug syndrome. Ib tug ntawm cov xeev - Banti lub syndrome.
feature
Hepato-splenic syndrome - nws yog tus thib ob lub npe ntawm tus mob no. Nws yog yus muaj los ntawm o ntawm daim siab thiab tus po, ntsig txog, cuam tshuam cov kabmob. Banti lub syndrome tshwm sim nyob rau hauv kab mob ntawm lub hepatobiliary system , thiab mob ntawm cov ntshav ncig nyob rau hauv lub "rooj vag Vienna - Vienna po."
Venous ntshav nyob rau hauv daim siab thiab tus po muab ib qho lus piav qhia txog yuav ua li cas cov kev cob cog rua lub cev thiab yuav ua li cas lawv muaj kev cuam tshuam rau txhua lwm yam nyob rau hauv xws li ib tug sib txawv li Banti syndrome. Koj muaj peev xwm taug venous kev twb kev txuas ntawm cov lub cev.
Tsev Vienna - yog lub portal. Nyob rau hauv nws cov ntshav yog sau los ntawm tus po thiab lwm yam kabmob ntawm lub plab kab noj hniav. Ces nws ntog mus rau hauv lub siab, qhov twg nws yog ntxuav ntawm cov teeb meem toxins thiab ces kis thoob plaws lub cev cov as-ham. Ib feem ntawm cov splenic portal cov hlab ntsha, tus po yog li ntawd nyob rau hauv ib tug heev nyob ze kev sib raug zoo nrog rau lub siab thiab cov txheej txheem uas tshwm sim nyob rau ntawd. Qhov no piav qhia yog vim li cas, nyob rau hauv Banti lub syndrome muaj feem xyuam rau lub siab thiab tus po.
Pathogenesis hepatolienal syndrome
ntshav teeb meem yuav ua tau vim narrowing ntawm lub lumen ntawm lub portal cov hlab ntsha. Muaj yog ib tug stagnation ntawm cov ntshav thiab raws li ib tug tshwm sim, ua rau kom nyob rau hauv cov ntshav siab. Yog vim li cas yog no mas? Ntawm no yog ib co yog vim li cas:
- Sab nraud compression ntawm lub portal cov hlab ntsha. Qhov no yuav tshwm sim ob tsis pub dhau lub siab, thiab lub hepatoduodenal nras nyob rau kev nkag mus rau lub cev. Nyob rau hauv cov ntaub ntawv no, soj ntsuam hepatolienal syndrome cov tsos mob yog tau nrog xws li cov kab mob:
- Mob npuas paug.
- Loj hauv daim ntawv ntawm tus kab mob siab.
- Thrombosis ntawm lub portal cov hlab ntsha thiab cov uas nyob ib sab loj leeg.
- Primary mob siab ntaub so ntswg.
- Plawv pathology ntawm txoj cai lub plawv.
- Biliary kab mob, hlav thiab cov hlwv.
- Hepatic cov hlab ntsha thrombosis.
2. narrowing ntawm lub lumen ntawm lub hlab ntsha:
- Thrombosis ntawm lub portal cov hlab ntsha thiab nws loj ceg.
- Hepatic cov hlab ntsha thrombosis, los yog Budd-Chiari syndrome.
Nyob rau hauv tas li ntawd mus ua lwm yam uas yuav ua rau o ntawm daim siab thiab tus po, qhov no tej zaum tseem tshwm sim raws li ib tug tiv thaiv cov tshuaj tiv thaiv mus rau lub ingress ntawm microbes.
theem
Muaj ntau ntau theem hepatolienal syndrome:
- Tus thawj theem yuav tshwm sim ib tug ob peb xyoos. Cov kev mob yog txaus siab, muaj yog ib tug me me anemia, leukopenia thiab neutropenia. Lub siab yog tsis tau nce, tab sis nws yuav ntau npaum li cas po.
- Qhov thib ob theem yog yus muaj los ntawm ib tug tseem ceeb nce nyob rau hauv lub siab. Muaj cov cim qhia ntawm nws cov functionality. Nws yuav kav rau ob peb lub hlis.
- Qhov thib peb theem. Nws ntev - kwv yees li ib xyoos. Yus zuj zus lawm lub siab thiab foob tsub kom ntshav liab tsawg, muaj cov cim qhia ntawm tawg, ascites, hnyuv los ntshav, esophageal varices.
- Qhov thib plaub theem. Characteristically cachexia, o, thiab los ntshav cov tsos mob.
ua rau
Feem ntau cov feem ntau, Banti lub syndrome nyob rau hauv cov me nyuam.
Cov ua rau cov menyuam yaus thiab cov neeg laus yuav tsum tau sib txawv:
- Mob muaj keeb kab mob.
- Kis kab mob.
- Congenital hemolytic anemia.
- Congenital thiab mas yuav kis tau tus kab mob ntawm cov portal cov hlab ntsha, splenic.
- Hemolytic kab mob ntawm tus me nyuam mos.
- Mob alcoholism.
uas yuav muaj pab pawg thiab sawv los ntawm cov tsos mob
Tag nrho cov kab mob uas yuav ua rau Banti lub syndrome yuav tau muab faib mus rau hauv pab pawg:
- Mob thiab mob siab. No pab pawg neeg yog yus muaj los ntawm kev mob los yog ib tug kev xav ntawm heaviness nyob rau hauv txoj cai hypochondrium, dyspeptic mob, pruritus, jaundice. Yog vim li cas tej zaum yuav ua tau kom ib tug kab mob kab mob siab, hu rau kab mob, phais kev pab los yog kev raug mob, kev haus dej caw, yeeb tshuaj txais tos gepatoksicheskih kis mob mob plab, kub ib ce.
- Cia cov kab mob. Lawv pom cov mej zeej ntawm lub tib lub tsev neeg los yog txheeb ze.
- Kis kab thiab cab kab mob. Nrog los ntawm ib tug zoo-txhais intoxication, kub taub hau, arthralgia, thiab myalgia.
- Cov kab mob ntawm cov hlab plawv system. Lawv nrog tachycardia, ischemicheskoy kab mob plawv, ib tug txuam nrog kua nyob rau hauv lub pericardial kab noj hniav, qhov kev nce thiab cov kev hloov nyob rau hauv lub configuration ntawm lub plawv.
- Kab mob ntawm cov ntshav thiab lymphoid cov ntaub so ntswg. Qhov no pab pawg neeg yog yus los ntawm xws li cov tsos mob li qaug zog, kub taub hau, o lymph node.
symptomatology
Yog hais tias muaj mob Banti lub syndrome, cov tsos mob tej zaum yuav muaj xws li:
- Nce siab thiab tus po. Mob rau palpation.
- Yuag.
- Nws cuam tshuam lub endocrine qog.
- Teeb meem nyob rau hauv lub digestive ib ntsuj av.
- Anemia. Pallor thiab qhuav daim tawv nqaij.
- Tau txuam nrog kua nyob rau hauv lub plab kab noj hniav.
- Nqaij thiab pob txha.
- Daj protein daim nyias nyias ntawm lub qhov muag.
- Tachycardia, ua tsis taus pa.
- Nkig rau tes, plaub hau poob.
Rau mob nws yog tsim nyog los dhau kev soj ntsuam, thiab rau ib tug ntau ncauj lus kom ntxaws tsom xam ntawm lub cev - mob.
diagnostics
Yog hais tias koj muaj kev saum toj no cov tsos mob differential mob ntawm hepatomegaly thiab hepatolienal syndrome. Ua li no, koj yuav tsum mus thov ib tug ntau yam ntawm kev ua ub no. Ib qho ntawm thawj cov ntsiab lus - ib tug general tsom xam ntawm cov ntshav thiab nws cov biochemical kev tshawb fawb. Yuav kom txiav txim yog vim li cas yog vim li cas muaj ib Banti lub syndrome, cov differential mob yog ib tug yuav tsum. Nws muaj:
- Sonography ntawm daim siab thiab tus po, tsib lub zais zis, mob plab hlab ntsha.
- Xoo tomography.
- PP lub siab thiab tus po.
- X-ray kev soj ntsuam ntawm lub duodenum.
- Laparoscopy.
- Punktsionalnaya me ntawm lub siab thiab tus po.
- Kev soj ntsuam ntawm lub hlwb pob txha thiab cov qog ntshav.
Tam sim no science yog tsis sawv tseem thiab yog lossi expanding lub cev nyob rau hauv lub mob ntawm xws li ib tug mob tsom xam raws li Banti lub syndrome. differential mob nrog rau lwm cov kab mob thiab cov kev soj ntsuam lub xeev ntawm lub siab yog tias muaj, nws yog ib lub ntsiab hauj lwm.
Kev Kho Mob thiab lwm yam mob ntawm tus kab mob
Raws li ib tug txoj cai, hepatolienal syndrome txoj kev kho no yog los qhia hais tias tus lwm tus kab mob thiab nws kho mob. Nws tsis yog ib qho kev ywj kab mob. Yog hais tias koj yog mob "Banti lub syndrome", cov kev kho mob yuav tsum muaj ib tug gastroenterologist. Nyob rau hauv cov ntaub ntawv no, siv gepatoprotektory, antivirals, cov tshuaj hormones thiab vitamins. Nyob rau hauv txhua rooj plaub, yuav tsum tau ib tug neeg mus kom ze, noj mus rau hauv tus account lub etiology ntawm tus kab mob.
Yog hais tias peb nco tus kab mob thiab tsis muaj kev kho, cov raug yuav ua tau disastrous. Cov teeb meem ntawm no syndrome - ib tug mob npuas paug ntawm lub siab, siab hlab ntsha thrombosis, o ntawm lub tsib lub zais zis, ntshav kab mob. Nyob rau hauv xws li mob, kev tshem tawm yuav siab feem thiab po los yog hloov khoom nruab nrog hloov thiab ntshav.
Nyob rau hauv thawj theem, cov neeg mob yuav tau mus ua hauj lwm thiab yuav mas ib tug me ntsis ce. Nyob rau hauv lub neej yav tom ntej, nrog rau lub deterioration ntawm qhov teeb meem no rau tus neeg mob yog tsis taus.
kev tiv thaiv
Nyob rau hauv kev txiav txim kom tsis txhob nco lub caij pib ntawm txoj kev loj hlob ntawm ib tug pathology, koj yuav tsum:
- Tsis tu ncua cov ntshav thiab zis kev ntsuam xyuas.
- Raws sij hawm pass kev soj ntsuam, tshwj xeeb tshaj yog yog hais tias koj muaj kev pheej hmoo.
- Kev tiv thaiv hepatolienal syndrome feem ntau muaj xws li combating ua ua rau lub siab mob thiab tus po.
- Nco ntsoov mus soj ntsuam cov Noj cov zaub mov rau cov khoom noj uas muaj qhov yuav tsum tau npaum li cas ntawm cov nqaijrog, cov nqaijrog thiab carbohydrates thiab, ntawm chav kawm, cov vitamins.
- Tsis txhob phem quav dej caw, kev haus luam yeeb thiab ua ib tug noj qab nyob zoo txoj kev ua neej.
Muaj yog tsis muaj txawm cov kab mob, tshwj xeeb tshaj yog yog hais tias lawv txheeb xws kabmob tseem ceeb heev raws li lub siab thiab tus po. Raws sij hawm kom paub tias cov teeb meem, thiab ces tus tsim nyog kho mob tau muab zoo tshwm sim.
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