Pituitary dwarfism. Yuav ua li cas yog nws?

Dwarfism los yog ncav, pituitary dwarfism, yog ib tug pathology nyob rau hauv uas muaj yog ncua sij hawm ntawm lub cev txoj kev loj hlob thiab kev loj hlob, uas yog tshwm sim los ntawm deficient synthesis thiab secretion ntawm kev loj hlob lawm (kuj hu ua txoj kev loj hlob hormone).

Qhov no pathology yog tsis tshua muaj tsis tshua muaj, nyob rau hauv thaj tsam li 2 tawm ntawm 10,000 cov neeg pituitary dwarfism yog kuaj nyob rau hauv ob ntau ntau nyob rau hauv cov tub hluas tshaj nyob rau hauv cov ntxhais. Txoj kev loj hlob nyob rau hauv cov txiv neej yog suav tias yog ntsias yog hais tias nws yog tsawg tshaj li 130 cm thiab rau cov poj niam tib yam - tsawg tshaj li 120cm.

Feem ntau qhov no yog cov nram qab no:

• yug tsis xws luag (nyob rau hauv utero anterior pituitary tsim incorrectly)

• taub hau raug mob (no muaj xws li ob qho tib si generic)

• pituitary mob los yog lwm tus lug,

• caj predisposition,

• syphilis, tuberculosis, sarcoidosis,

• kis raws li cov kws khomob los yog tawg txoj kev kho.

Txawm li cas los, ntau tshaj ib nrab ntawm cov ua dwarfism thiab nyob twj ywm lam.

Raws li cov pituitary dwarfism muaj?

Nyhav thiab qhov siab ntawm cov me nyuam nrog tsis txaus secretion ntawm kev loj hlob lawm nyob rau hauv yug me nyuam tsis txawv los ntawm lub sib nug xov tseem ceeb ntawm kev noj qab nyob cov me nyuam. thawj tsos mob feem ntau tshwm sim nyob rau hauv cov me nyuam kom txog rau thaum lub hnub nyoog ntawm 2-3 xyoo: cov me nyuam tsis pib kom tau mus nrog cov qub kev loj hlob ntawm lawv cov phooj ywg. Sharply txo txoj kev loj hlob nqi, uas tsis pub tshaj 3.4 cm / xyoo (ntawm ib tus nqi ntawm kwv yees li 8 cm / yr). Txawm tias qhov kev ncua ntawm txoj kev loj hlob, qhov tseeb proportions ntawm lub cev ntawm tus me nyuam yog khaws cia.

Nyob rau hauv tas li ntawd, pituitary insufficiency li manifested los ntawm cov nram qab no nta:

• underdevelopment ntawm lub tsev me nyuam system,

• muab sau underdeveloped npag system,

• hypotension,

• Txo cov kev ceev ntawm ossification ntawm lub cev pob txha, tawg hniav kev loj hlob thiab kev hloov,

• Yog hais tias muaj yog ib tug mob nyob rau hauv lub pituitary caj pas los yog lub cheeb tsam surrounding ntawm lub paj hlwb, nyob rau hauv Ntxiv rau cov tsos mob, nws tsim ntau thiab qhov muag plooj tsis pom kev.

Feem ntau, lub hlwb txoj kev loj hlob nyob rau hauv tus kab mob no tsis raug kev txom nyem, cov neeg mob feem ntau yog muaj zoo cim xeeb.

.Yuav paub meej tias qhov mob ntawm "pituitary dwarfism" yog tsim nyog:

• soj ntsuam kev loj hlob lawm. Nyob rau hauv tas li ntawd, tej zaum koj yuav xav tau kev ntsuam xyuas kom paub tias lwm cov tshuaj hormones. Tej zaum koj yuav tsum hormonal kev ntsuam xyuas: thawj txiav txim siv theem ntawm cov tshuaj hormones rau hauv cov ntshav, tom qab uas tus neeg mob yuav siv sij hawm ib tug tshuaj uas muaj feem xyuam rau cov kev cai ntawm lawm, tom qab ib tug tej lub sij hawm, tus tsom xam yog rov qab.

• Khiav X-ray cheeb tsam ntawm Sella thiab pob txha taub hau los mus txiav txim qhov loj ntawm lub pituitary caj pas. Tsis tas li ntawd hais tuav lub computer los yog sib nqus resonance imaging ntawm lub paj hlwb, yog ib tug mob txoj kev, lawv tso cai rau koj mus saib lub meej qhov chaw nyob ntawm lub pituitary cheeb tsam thiab puag ncig lub hlwb cov ntaub so ntswg. Yog hais tias muaj yog deterioration ntawm lub zeem muag, nws yog tseem tsim nyog mus tham ib tug ophthalmologist.

Pituitary dwarfism kho los ntawm endocrinologists. Cov yooj yim txoj kev ntawm es txoj kev loj hlob lawm ntau ntau nyob rau hauv lub cev yog hloov txoj kev kho: siv ntawm mus tas li dag loj lawm. Yuav kom pab txhawb lub xam ntawm lub ntau npaum thiab tswj ntawm kev loj hlob lawm yog tam sim no tsim ib tug tshwj xeeb cwj mem cov kev txhaj tshuaj.

Yog hais tias tsim nyog kho mob yog ib qho kev nce rau hauv txoj kev loj hlob npaum li cas mus rau li qub ntau ntau (8-12 cm / xyoo), ua ntej rau kev kho mob, raws li ib tug txoj cai, muaj tsuas yog 3-4 cm / xyoo. Thaum lub sij hawm tiav nkauj tiav nraug yuav tsum tau muaj nyob rau hauv cov kev kho mob regimen nrog txiv neej pw cov tshuaj hormones.

Cov hauj lwm zoo ntawm kev kho mob nyob rau cov ua ntawm tus kab mob, nws tau tshwm sim los. Feem ntau cov feem ntau, cov neeg mob uas txaus kho mob mus txog li qub kev loj hlob thiab hloov mus rau cov ib puag ncig.

Xa mus rau cov kws txawj nyob rau hauv cov thawj cov cim qhia ntawm pituitary insufficiency!