Noj qab haus huv, Cov kab mob thiab mob
Amniotic constriction: ua, cov tsos mob, mob, thiab kev kho mob regimen
Tej zaum clinically noj qab nyob zoo niam muab yug rau cov me nyuam mos nrog morphological tsis xws luag: tsis muaj phalanges, ceg ntoo thiab txawm hau. Cov niam yog nyob rau hauv tag kev cia siab, liam tias nws tus kheej los yog cov kws kho mob dab tsi tau tshwm sim rau lawv tus me nyuam. Tej zaum nws los txog rau mus sib hais. Tab sis zoo li cas tiag yog qhov ua rau ntawm kev yug me nyuam tsis xws luag?
txhais
Amniotic constriction, txwv tsis pub hu ua "amniotic leeg" los yog "strands Simonara" sawv cev dublication amnion ntaub uas yog ncav us txog ntawm lub uterine phab ntsa. Raws li ib tug txoj cai, nws tsis ua mob rau tus embryo thiab tsis ua rau mob nyob rau hauv me nyuam. Tab sis nyob rau hauv uas tsis tshua muaj mob, yuav ua nyob rau hauv loj qhov yuav tshwm.
Amniotic constriction - fiber filaments, uas tshwm sim nyob rau hauv lub me nyuam hauv plab zais zis. Tej zaum lawv yuav hlob los yog ntaub qhwv txoj hlab ntaws txuas mus rau qhov chaw ntawm lub cev ntawm lub fetus, ua yug tsis xws luag (amputation ntawm ob txhais tes, ob txhais taw, ntiv taw, los yog phalanges, tej zaum tus kheej tus tub).
yog vim li cas
Muaj ob theories yog vim li cas muaj amniotic constriction. Yog vim li cas rau qhov no tshwm sim piav txog cov nquag ruptures amniotic npuas nyob rau hauv thaum ntxov cev xeeb tub. Raws li cov chorion tseem lawm, lub kev hem thawj ntawm kev cuam tshuam ntawm embryo txoj kev loj hlob yog tsis pom, tab sis cov xov uas tshwm sim vim so, free-floating nyob rau hauv lub amniotic kua. Lawv yuav tsum tau ua ke rau hauv lub cev ntawm lub txiv hmab txiv ntoo. Nyob rau hauv lub chav kawm ntawm lub cev xeeb tub tus me nyuam loj hlob, tab sis cov xov tseem tib yam li lawv, thiaj li muaj compression ntawm cov ntaub so ntswg ischemia thiab necrosis.
Tej lub sij hawm tom qab, ib tug thib ob lub hom phiaj, raws li cov thawj tsis siav skeptics uas pom tias amniotic constriction (cov hlua nyob rau hauv lub plab ntawm ib tug cev xeeb tub poj niam) yuav tshwm sim ib txhij nrog lwm congenital malformations xws li cleft di ncauj los yog cleft palate. Cov kws kho mob tau pom hais tias muaj bands vim vascular mob los yog mob ntawm me nyuam hauv plab ncig.
Lwm version ntawm cov txheej xwm yog intrauterine tus kab mob, thiab raug mob thaum lub sij hawm cev xeeb tub, kev txawv txav genitalia (doubling ntawm lub tsev me nyuam, ob-horned lub tsev me nyuam , thiab hais txog. D.), CIN (lub tsev me nyuam incompetence), o ntawm lub amnion, endometritis, oligohydramnios. Tab sis tsis muaj leej twg ntawm cov theories tau paub tseeb hais tias conclusively.
diagnostics
Nyob rau hauv feem ntau tus neeg mob, soj ntsuam thiab kuaj tsis qhia hais tias yuav amniotic constriction. Duab los ntawm lub ultrasound txoj kev tshawb no uninformative, txij li thaum cov threads yog heev nyias. Kov koj yuav paub mob thiab o nqua nyob rau hauv qhov chaw ntawm compression. Lom zem ntau ntau overdiagnosis ntawm no pathology. Yog li ntawd, yog tias ib tug kws kho mob yog xav tias muaj cov amniotic bands, cev xeeb tub raws kev coj kom MRI thiab 3D ultrasound.
Ntau tshaj ib nrab ntawm thiaj paub hais tias amniotic constrictions rau rov ultrasound yuav tsis yuav ntes tau vim lawv kev sib tawg.
statistics
Nyob ntawm seb cov kev khoom prenatal zaus uas cov kuaj amniotic constrictions tej zaum yuav txawv ntawm 1: 1200 rau 1:15 000 genera. Nws yog ntseeg hais tias ob puas thiab kaum txhiab abortions tshwm sim rau no yog vim li cas. Eighty feem pua ntawm cov strands Simonara deform tus ntiv tes thiab ob txhais tes, thiab lwm kaum feem pua - ib tug compression ntawm txoj hlab ntaws. Uas tsim los ntawm cov pob caus ntawd nyob rau hauv txoj hlab ntaws ua rau hypoxia thiab antenatal me nyuam hauv plab tuag.
Qhov zoo ces, feem ntau mob "amniotic band constriction" yog tsis txaus siab los ntawm kev soj ntsuam los yog fibrous strands tsis ua teeb meem loj mob mus rau lub fetus.
caj
Qhov ntau hais tias tus amniotic constrictions tshwm sim thaum lub sij hawm cev xeeb tub, yog tsis tshua muaj me me. Qhov no yog tsis yog ib tug raws roj ntsha kab mob. Feem ntau, cov genomic los yog chromosomal change tshwm sim symmetrically, thiab nyob rau hauv cov ntaub ntawv no, cov xov txuas kiag li random. Yog hais tias tus thawj uas cev xeeb tub nyob rau hauv tus me nyuam kawm Simonara cai, nws tsis txhais hais tias tom ntej cov me nyuam yuav tsum raug mob. Tsis tas li ntawd, nws tsis txhais hais tias cov niam txiv uas tau raug kev txom nyem nyob rau hauv utero amniotic band constriction, ib tug me nyuam yug los nrog malformations.
los
Txawm tias amniotic constrictions - yog tsis tuag pathology, cov teebmeem ntawm nws yog heev disappointing. Vim lub fact tias cov bands yuav entangle me nyuam hauv plab qhov chaw ntawm lub cev, kev tsim qog stagnation. Qhov no ua rau edema thiab necrosis. Tom qab tus me nyuam yug ntawm xws li ib tug povtseg yuav tsum tau amputated, los yog tsim zuaj-syndrome: cov co toxins uas tau sau nyob rau hauv anesthetized povtseg, lub caij nplooj zeeg mus rau hauv lub mauj kev thiab kabmob yuav pib mus rau tshuaj lom rau tus me nyuam. Qhov no yuav ua rau nws txoj kev tuag. Nws yog yog li ntawd tsim nyog los tshem tawm cov povtseg, yog hais tias nws yog twb unsustainable. Thiab sai li sai tau.
Nyob rau hauv tas li ntawd, nyob rau hauv lub syndrome ntawm amniotic constrictions yuav depressions ceg ntoo thiab cov ntiv tes mus rau hauv lub proximal ib feem ntawm lub limb. Nquag nrog cov me nyuam leeg toes los yog phalanges ntawm cov ntiv tes thiab ntiv taw. Tej zaum, nyob rau hauv tas li ntawd mus rau lub constrictions ntawm tus me nyuam muaj cai lwm yam stigma disembriogeneza: cleft palate thiab lub Upper di ncauj. Nyob rau hauv tsis tshua muaj heev neeg mob muaj tag nrho cov kev ua txhaum ntawm cov nqaj qaum thiab lub ntsej muag pob txha taub hau, eventration mob plab kabmob, atresia ntawm txoj hlab ntaws.
Yog hais tias constriction muaj feem xyuam rau zoo spaced receptacles rau ntawm daim tawv nqaij, ces thaum no nws yog tsim hemangioma. Pob tom qab yug tus me nyuam yuav tsum tau muab tshem tawm.
Tej zaum nrhiav tau kev twb kev txuas cords Simonara nrog clubfoot. Qhov no yog vim hais tias cov me nyuam hauv plab ob txhais ceg yog tsau fiber strands, li ntawd, lub tsev menyuam yuav hlob tus taw ntawm lub fetus. Nees nkaum feem pua ntawm no pathology yog ob mog. Lwm kev pheej hmoo, uas yuav tsum tau muab ib tug obstetrician - yog ntxov ntxov yug. Qhov no yam tab kaum - ib tug heev tshwm sim nyob rau hauv me nyuam uas tshwm sim nrog rau syndrome amniotic constrictions.
kev kho mob
Raws li ib tug txoj cai, nyob rau hauv utero yog ib tug kab mob yuav kho tsis zoo. Nyob rau hauv kev kho mob xyaum, muaj anecdotal mob qhov twg ib tug transvaginal los yog laparoscopic phais. Tab sis nws yog ib tug huab ntsuas, raws li pinched siab ntsws tseem ceeb. Tab sis nws yog tsis tshua muaj heev amniotic constriction. Kev kho mob feem ntau yog nqa tawm tom qab tus me nyuam yug los.
Lub fibers yog dissected thiab amputated ib feem ntawm ib tug povtseg yog tias tsim nyog. Yuav kom txhim kho txoj kev zoo ntawm lub neej yuav tsum transplanted ntiv tes cia nws caj npab.
outlook
Cov raug rau lub neej thiab noj qab haus huv, yog feem ntau paaj. Cov me nyuam nyob rau hauv feem ntau loj hlob thiab kev loj hlob raws li lub hnub nyoog. Txhua xyoo lub nqua zoo, yog li koj tsis tau kev forearm, tes, txo ceg los yog ko taw yog ua tau rau sau ib co kev hloov. Cov me nyuam yuav xav kom hloov cov hniav cuav raws li lawv loj hlob lawm. Yog hais tias lub constriction tshwm sim los me haumxeeb kho raws, kom hniav zoo nkauj kho raws tau muab tshem tawm los ntawm hloov lwm lub tsev ntiv tes thiab lawv phalanges.
Nyob rau hauv cov neeg uas muaj lub syndrome amniotic constrictions yuav tau yug txig noj qab nyob zoo cov me nyuam, raws li tus kab mob no yog tsis pub.
Celebrities uas tau muaj bands Simonara
Nws tau ib lub sij hawm thaum cov neeg uas muaj povtseg amputation tau nkaum nyob rau hauv lawv tsev neeg thiab ostracized los ntawm haiv neeg. Tam sim no lawv muaj peev xwm nyob nrog zoo tsis muaj kev txwv, los tuav ib qho tseem ceeb rau pej xeem txaus qhia, kev siv zog, tshwm nyob rau hauv TV thiab koom nyob rau hauv kev zoo nkauj kev sib tw.
Ib txhia nto moo tus neeg yeej tsis txaj muag ntawm kev yug nrog congenital amputation, tab sis seb uas yog vim amniotic constriction - ib qhib rau lo lus nug.
- Carrie Bornell - actress, uas tau yug los tsis muaj ib tug cai forearm. Nws ua haujlwm rau cov me nyuam lub TV channel. Qhov no tshwm sim los ib tug tov cov tshuaj tiv thaiv cov tub ntxhais hluas viewers thiab lawv niam lawv txiv, thiab muab impetus mus rau lub rov tshwm sim ntawm ib tug series ntawm cov kev pab cuam txog yuav ua li cas qhia cov me nyuam txog kev xiam oob qhab thiab nta tshwj xeeb ntawm lub neej ntawm cov neeg no.
- Dzhim Ebbot yog paub rau tag nrho cov kiv cua ntawm baseball. Nws yog ib tug legendary tshob rau dej, piv txwv li pub, tsis muaj txoj cai txhuam. Nws so los ntawm kev ua si nawv nyob rau thaum xaus ntawm lub thib nees nkaum xyoo pua, tab sis nws tus yam ntxwv tseem txhawb ntau cov neeg uas muaj kev tsis taus thiab Paralympians.
- Teresa yukata - ib tug zoo nkauj Miss America, twb yug los tsis muaj ib tug sab laug tes. Thaum lub sij hawm sib tw, kuv tsis hnav ib prosthesis, los qhia tau tias koj yuav ua tau zoo nkauj thiab tsis muaj dag qhov chaw.
- Kelli Noks - sab saum toj qauv tsis muaj ib tug laug forearm. Nyob rau hauv 2008, nws yeej muaj tiag qhia rau cov BBC channel 3. Nyob rau hauv tas li ntawd mus rau nws nyob rau hauv qhov kev sib txeeb muab kev koom tes xya ntxhais uas muaj ntau yam kev tsis taus.
- Nikolas Makkarti - renowned pianist, uas tau yug los tsis muaj ib tug sab tes xis.
- Nikolas Vuychich - Australian Christian qhia Vajtswv lus. Nto moo rau yug tsis muaj nqua. Nws luam tawm nws cov phau ntawv thiab mus rau seminars tag nrho cov thoob lub ntiaj teb no raws li ib qho piv txwv, hais tias koj yuav tsum tsis txhob muab li txawm nyob rau hauv lub feem ntau nyuaj teeb meem.
- Mark Goffeni - guitarist, yug nrog amputated ob txhais tes. Nws kawm tau mus ua si nrog nws cov ntiv taw.
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